Heerfordt-Waldenström syndrome is a rare subacute variant of sarcoidosis, characterized by enlargement of the parotid or salivary glands, facial nerve paralysis. Images in Clinical Medicine from The New England Journal of Medicine — Heerfordt’s Syndrome, or Uveoparotid Fever. Heerfordt’s syndrome is a rare manifestation of sarcoidosis characterized by the presence of facial nerve palsy, parotid gland enlargement.

Author: Arashirg Brakazahn
Country: Rwanda
Language: English (Spanish)
Genre: Art
Published (Last): 11 September 2014
Pages: 397
PDF File Size: 10.65 Mb
ePub File Size: 13.3 Mb
ISBN: 872-6-56922-902-8
Downloads: 88021
Price: Free* [*Free Regsitration Required]
Uploader: Fenrizahn

CT of the neck soft tissues demonstrating prominent cervical lymphadenopathy. No rashes were noted.

Angiotensin I-converting enzyme ACE for sarcoidosis diagnosis. Facial palsy in Heerfordt’s syndrome: Treatments for sarcoidosis include corticosteroids and immunosuppressive drugs. View at Google Scholar J. No nodules were heefordt and diffuse swelling of parotid gland was observed in the US examination.

Tender, mobile submandibular and cervical lymph nodes were palpable bilaterally, but more prominently on the left. Christian Heerfordt first described this constellation of symptoms in He was admitted to the Department of Dermatology in our hospital in August, because of worsening swelling of his right eyelid.

Oral corticosteroids represent the first line treatment option. Three patients had the full form, 13 had the incomplete form, and all had uveitis. In tuberculosis, the mastoid, middle ear, or petrous bone is often involved 12. Journal List An Bras Dermatol v.


Table of Contents Alerts. Radiologic manifestations of sarcoidosis in various organs. Larissa Karine Leite Portocarrero, Av. Journal of the American Academy of Physician Assistants. Although uveitis was not detected in the ophthalmologic examination, biopsy specimens from the right eyelid and the lymph node in the left thigh revealed syndrpme epithelioid cell granuloma and a diagnosis of sarcoidosis was made histologically Figure 3.

National Center for Biotechnology InformationU. Nerve granulomas and vasculitis in sarcoid peripheral neuropathy: After three months, the patient developed a cough, chest pain and dyspnea and was admitted for investigation.

Heerfordt syndrome

To receive news and publication updates for Case Reports in Otolaryngology, enter your email address in the box below. He presented with a regular general status. Current approach in diagnosis and management of anterior uveitis.

Received Sep 30; Accepted Jul The authors declare that there is no conflict of interests regarding the publication of this paper. A year-old woman visited our hospital due to left facial palsy and bilateral hearing loss lasting for heerforddt days.

This patient had marked improvement of symptoms after sydnrome days of prednisone therapy. Diagnosis of Heerfordt’s syndrome by state-of-the-art ultrasound in combination with parotid biopsy: Possible associated diseases need independent treatment 3. Prominent hilar markings were identified on chest x-ray, but no focal opacity was seen.


Support Radiopaedia and see fewer ads. Fine-needle aspiration of a left preauricular lymph node revealed multinucleated giant cells and noncaseating granulomas consistent with granulomatous lymphangitis Figure 2.

Some observations of uveoparotitis and allied conditions with special reference to the symptoms from the syndro,e system. Cranial nerve palsy in neurosarcoidosis may be caused by nerve granulomas, perineural inflammatory infiltrates, increased cranial pressure, or granulomatous basal meningitis [ 11syndorme ].

Case Reports in Otolaryngology. Serum ACE and sIL-2R levels were elevated; however, there was no significant elevation in serum antibody for varicella zoster virus.

However, the patient required urgent hospitalization for heart failure after 2 months. Find articles by Neusa Yuriko Sakai Valente. No recurrence has been observed to date.

[Heerfordt syndrome].

Rheumatoid factor was not checked on initial presentation. N Engl J Med.

Although it usually affects the lung, any organ may be syncrome. Orofacial presentations of sarcoidosis—a case series and review of the literature. Physical examination revealed a swollen left cheek and left facial droop involving the forehead, cheek, and chin.

Sarcoidosis D86 ,